Source Code Name Case count Share of cases (%)
OUTPAT OUTPAT_ICD10(Q8500) Neurofibromatosis, type 1 249
OUTPAT OUTPAT_ICD10(Q8509) Unspecified neurofibromatosis 165
INPAT INPAT_ICD10(Q8500) Neurofibromatosis, type 1 120
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8500) Neurofibromatosis, type 1. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 101
OUTPAT OUTPAT_ICD10(Q851) Tuberous sclerosis 74
OUTPAT OUTPAT_ICD10(Q8501) Neurofibromatosis, type 2 66
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q850) Neurofibromatosis (nonmalignant). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 65
INPAT INPAT_ICD10(Q8509) Unspecified neurofibromatosis 58
OUTPAT OUTPAT_ICD10(Q850) Neurofibromatosis (nonmalignant) 52
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8509) Unspecified neurofibromatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 48
INPAT INPAT_ICD10(Q851) Tuberous sclerosis 37
OUTPAT OUTPAT_ICD10(Q8582) of Hipple-Lindau syndrome 31
INPAT INPAT_ICD10(Q8501) Neurofibromatosis, type 2 29
OUTPAT OUTPAT_ICD10(Q859) Phakomatosis, unspecified 28
INPAT INPAT_ICD10(Q850) Neurofibromatosis (nonmalignant) 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q851) Tuberous sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 24
INPAT INPAT_ICD10(Q8582) of Hipple-Lindau syndrome 17
OUTPAT OUTPAT_ICD10(Q8580) Peutz-Jegher syndrome 15
OUTPAT OUTPAT_ICD10(Q8588) Other phakomatoses, not elsewhere classified 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8501) Neurofibromatosis, type 2. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8582) of Hipple-Lindau syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
OUTPAT OUTPAT_ICD10(Q8581) Sturge-Weber syndrome 10
DEATH DEATH_ICD10(Q850) Neurofibromatosis (nonmalignant) 9
INPAT INPAT_ICD10(Q859) Phakomatosis, unspecified 9
OUTPAT OUTPAT_ICD10(Q8583) Gardner syndrome 9
INPAT INPAT_ICD10(Q8580) Peutz-Jegher syndrome 8
INPAT INPAT_ICD10(Q8581) Sturge-Weber syndrome 8
INPAT INPAT_ICD10(Q8588) Other phakomatoses, not elsewhere classified 7
DEATH DEATH_ICD10(Q858) Name not found 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(Q8581) Sturge-Weber syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5