| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 1319 | |
| INPAT | INPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 775 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 568 | |
| OUTPAT | OUTPAT_ICD10(M313) | Wegener's granulomatosis | 553 | |
| INPAT | INPAT_ICD10(M313) | Wegener's granulomatosis | 395 | |
| OUTPAT | OUTPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 255 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M313) | Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 230 | |
| OUTPAT | OUTPAT_ICD10(M317) | Microscopic polyangiitis | 207 | |
| INPAT | INPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 153 | |
| INPAT | INPAT_ICD10(M317) | Microscopic polyangiitis | 142 | |
| OUTPAT | OUTPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 128 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M317) | Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 74 | |
| INPAT | INPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 72 | |
| OUTPAT | OUTPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 68 | |
| INPAT | INPAT_ICD9(4476A) | Arteritis, unspecified | 61 | |
| DEATH | DEATH_ICD10(M313) | Wegener's granulomatosis | 45 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M319) | Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 45 | |
| INPAT | INPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 39 | |
| INPAT | INPAT_ICD8(44698) | Polyarteritis nodosa and allied conditions, Other | 33 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M314) | Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 29 | |
| INPAT | INPAT_ICD9(4464A) | Wegener's granulomatosis | 24 | |
| DEATH | DEATH_ICD10(M317) | Microscopic polyangiitis | 23 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M318) | Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 20 | |
| INPAT | INPAT_ICD9(4467A) | Takayasu's disease | 9 | |
| DEATH | DEATH_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 8 | |
| DEATH | DEATH_ICD10(M319) | Necrotizing vasculopathy, unspecified | 7 | |
| INPAT | INPAT_ICD8(44620) | Polyarteritis nodosa and allied conditions, Other hypersensitivity angiitis | 6 |